D70.0

Applicable To

• Congenital neutropenia

• Infantile genetic agranulocytosis

• Kostmann’s disease

Approximate Synonyms

• Congenital neutropenia

• Neutropenia, congenital

Clinical Information

• A rare disorder characterized by recurrent infantile infections and absence of neutrophils in the peripheral blood.

• An inherited disorder in which there is a lower-than-normal number of neutrophils a type of white blood cell that is important in fighting infections). Infants with the disorder get infections caused by bacteria, and are at an increased risk of acute myelogenous leukemia aml) or myelodysplasia a bone marrow disorder).

Details

• D70.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

• The 2023 edition of ICD-10-CM D70.0 became effective on October 1, 2022.

• This is the American ICD-10-CM version of D70.0 – other international versions of ICD-10 D70.0 may differ.