Congenital NADH-methemoglobin reductase deficiency
Hemoglobin-M [Hb-M] disease
Methemoglobinemia, hereditary
Methemoglobinemia inherited in an autosomal recessive pattern. It is caused by deficiency of the enzyme nadh methemoglobin reductase or the presence of abnormal hemoglobin m. It presents with cyanosis early in life. There is no evidence of cardiopulmonary disease present.
D74.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2023 edition of ICD-10-CM D74.0 became effective on October 1, 2022.
This is the American ICD-10-CM version of D74.0 – other international versions of ICD-10 D74.0 may differ.