G12.0
Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
Approximate Synonyms
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Werdnig hoffmann disease
Clinical Information
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The most severe form of spinal muscular atrophy. It is manifested in the first year of life with muscle weakness, poor muscle tone, and lack of motor development. The motor neuron death affects the major organ systems, particularly the respiratory system. Most patients die before the age of two secondary to pneumonia.
Details
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G12.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
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The 2023 edition of ICD-10-CM G12.0 became effective on October 1, 2022.
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This is the American ICD-10-CM version of G12.0 – other international versions of ICD-10 G12.0 may differ.