C83.0

Applicable To

• Lymphoplasmacytic lymphoma

• Nodal marginal zone lymphoma

• Non-leukemic variant of B-CLL

• Splenic marginal zone lymphoma

Clinical Information

• A b-cell non-hodgkin lymphoma composed of small lymphocytes which surround and replace the splenic white pulp germinal centers. It involves the spleen and splenic hilar lymph nodes, bone marrow, and often the peripheral blood. When lymphoma cells are present in the peripheral blood, they are usually, but not always, characterized by the presence of short polar villi. Patients present with splenomegaly and the clinical course is indolent. who)

• A clonal neoplasm of small b-lymphocytes, lymphoplasmacytoid cells, and plasma cells involving the bone marrow, lymph nodes, and the spleen. The majority of patients have a serum igm paraprotein.

• A malignant neoplasm composed of lymphocytes b-cells), lymphoplasmacytoid cells, and plasma cells.

• A primary nodal b-cell non-hodgkin lymphoma which morphologically resembles lymph nodes involved by marginal zone lymphomas of extranodal or splenic types, but without evidence of extranodal or splenic disease. This is a rare entity, and most patients present with localized or generalized lymphadenopathy. The clinical course is indolent. who, 2001)

• An indolent slow-growing) type of non-hodgkin lymphoma marked by abnormal levels of igm antibodies in the blood and an enlarged liver, spleen, or lymph nodes.

Details

• C83.0 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.

• The 2023 edition of ICD-10-CM C83.0 became effective on October 1, 2022.

• This is the American ICD-10-CM version of C83.0 – other international versions of ICD-10 C83.0 may differ.