Intravascular large B-cell lymphoma
Lymphoid granulomatosis
Primary effusion B-cell lymphoma
A neoplastic lymphoproliferative process characterized by an angiocentric arrangement of the tumor cells which is associated with angiodestruction. It includes lymphomatoid granulomatosis which is a lymphoproliferative lesion derived from mature b-lymphocytes and cases of extranodal nk/t-cell lymphomas of nasal type.
A rare extranodal b-cell non-hodgkin lymphoma, characterized by the presence of lymphoma cells exclusively in the lumina of small vessels, particularly capillaries. This is an extremely aggressive lymphoma which responds poorly to chemotherapy. who, 2001)
An angiocentric and angiodestructive lymphoproliferative disease involving extranodal sites, comprised of epstein-barr virus ebv)-positive b-cells admixed with reactive t-cells. Incidence is higher among adult males; patients with a history of immunodeficiency are at increased risk. The most common site of involvement is the lung; other common sites include brain, kidney, liver, and skin. Morphologically, three grades are recognized: grade i, ii, and iii. Grade iii lymphomatoid granulomatosis should be approached clinically as a subtype of diffuse large b-cell lymphoma.
An angiocentric and angiodestructive lymphoproliferative disorder primarily involving the lungs. It is caused by an epstein-barr virus-induced transformation of the b-cells, in a t-cell rich environment. Clinically and pathologically it resembles extranodal nk-t-cell lymphoma.
Destructive growth of lymph cells, usually involving the lungs, skin, kidneys, and central nervous system. Grades i and ii are not considered cancerous, but grade iii is considered a lymphoma.
C83.8 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
The 2023 edition of ICD-10-CM C83.8 became effective on October 1, 2022.
This is the American ICD-10-CM version of C83.8 – other international versions of ICD-10 C83.8 may differ.