Acholuric familial) jaundice
Congenital spherocytic) hemolytic icterus
Minkowski-Chauffard syndrome
Spherocytosis, hereditary
A familial congenital hemolytic anemia characterized by numerous abnormally shaped erythrocytes which are generally spheroidal. The erythrocytes have increased osmotic fragility and are abnormally permeable to sodium ions.
An autosomal dominant inherited disorder characterized by the presence of smaller than normal, sphere-shaped erythrocytes. It results in hemolytic anemia and splenomegaly.
Autosomal dominant trait marked by splenomegaly, jaundice, and fragile, spheroid erythrocytes which are prematurely cleared by the spleen; anemia is usually mild; treatment is splenectomy.
D58.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2023 edition of ICD-10-CM D58.0 became effective on October 1, 2022.
This is the American ICD-10-CM version of D58.0 – other international versions of ICD-10 D58.0 may differ.