D76.3

Applicable To

• Reticulohistiocytoma giant-cell)

• Sinus histiocytosis with massive lymphadenopathy

• Xanthogranuloma

Approximate Synonyms

• Acute histiocytosis

• Chronic histiocytosis

• Hemophagocytic syndrome

• Hemophagocytic syndromes

• Histiocytic syndrome

• Histiocytosis

• Histiocytosis, acute

• Histiocytosis, chronic

• Histiocytosis, undetermined cell

• Juvenile xanthogranuloma

• Langerhans cell histiocytosis, disseminated clinical)

• Rosai dorfman syndrome

• Sinus histiocytosis with massive lymphadenopathy

• Undetermined cell histiocytosis

• Xanthogranuloma

Clinical Information

• A morphologic finding indicating the presence of histiocytic infiltrates within distended lymph node sinuses.

• A rare non-neoplastic disorder of unknown etiology characterized by distention of the lymph node sinuses and sinusoidal histiocytic infiltration. The histiocytes characteristically contain ingested lymphocytes. It is usually manifested with cervical lymphadenopathy, fever, leukocytosis, and hypergammaglobulinemia. . it can affect extranodal sites, including the skin, bones, and the respiratory tract. It usually regresses spontaneously.

• Benign, non-langerhans-cell, histiocytic proliferative disorder that primarily affects the lymph nodes. It is often referred to as sinus histiocytosis with massive lymphadenopathy.

• Condition of faulty lipid metabolism in which yellow nodules of lipoid matter are deposited in the skin and mucosae, giving rise to granulomatous reactions.

Details

• D76.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

• The 2023 edition of ICD-10-CM D76.3 became effective on October 1, 2022.

• This is the American ICD-10-CM version of D76.3 – other international versions of ICD-10 D76.3 may differ.