D81.81
Biotin-dependent carboxylase deficiency
Applicable To
-
Multiple carboxylase deficiency
Clinical Information
-
A deficiency in the activities of biotin-dependent enzymes propionyl-coa carboxylase, methylcrotonyl-coa carboxylase, and pyruvate carboxylase) due to one of two defects in biotin metabolism. The neonatal form is due to holocarboxylase synthetase deficiency. The late-onset form is due to biotinidase deficiency.
Details
-
D81.81 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
-
The 2023 edition of ICD-10-CM D81.81 became effective on October 1, 2022.
-
This is the American ICD-10-CM version of D81.81 – other international versions of ICD-10 D81.81 may differ.