Multiple carboxylase deficiency, unspecified
Biotin dependent carboxylase deficiency
A deficiency in the activities of biotin-dependent enzymes propionyl-coa carboxylase, methylcrotonyl-coa carboxylase, and pyruvate carboxylase) due to one of two defects in biotin metabolism. The neonatal form is due to holocarboxylase synthetase deficiency. The late-onset form is due to biotinidase deficiency.
D81.819 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2023 edition of ICD-10-CM D81.819 became effective on October 1, 2022.
This is the American ICD-10-CM version of D81.819 – other international versions of ICD-10 D81.819 may differ.