D89.82

Approximate Synonyms

• Autoimmune lymphoproliferative syndrome

Clinical Information

• An autoimmune hematologic disorder characterized by autoimmune hemolytic anemia, thrombocytopenia, lymphadenopathy, hepatomegaly and splenomegaly. Patients are at an increased risk of developing hodgkin and non-hodgkin lymphomas.

• Rare congenital lymphoid disorder due to mutations in certain fas-fas ligand pathway genes. Known causes include mutations in fas, tnfsf6, nras, casp8, and casp10 proteins. Clinical features include lymphadenopathy; splenomegaly; and autoimmunity.

Details

• D89.82 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

• The 2023 edition of ICD-10-CM D89.82 became effective on October 1, 2022.

• This is the American ICD-10-CM version of D89.82 – other international versions of ICD-10 D89.82 may differ.