E31.0

Applicable To

• Schmidt’s syndrome

Approximate Synonyms

• Autoimmune polyendocrinopathy

• Lloyd syndrome

• Polyglandular autoimmune syndrome, type 2

• Schmidts syndrome

Clinical Information

• A rare genetic syndrome characterized by autoantibodies production against more than one endocrine organ. The range of endocrinopathies includes hypoparathyroidism, adrenal insufficiency, hypogonadism, type 1 diabetes mellitus and hypothyroidism.

• An autoimmune diseases affecting multiple endocrine organs

• Autoimmune diseases affecting multiple endocrine organs. Type i is characterized by childhood onset and chronic mucocutaneous candidiasis candidiasis, chronic mucocutaneous), while type ii exhibits any combination of adrenal insufficiency addison’s disease), lymphocytic thyroiditis thyroiditis, autoimmune;), hypoparathyroidism; and gonadal failure. In both types organ-specific antibodies against a variety of endocrine glands have been detected. The type ii syndrome differs from type i in that it is associated with hla-a1 and b8 haplotypes, onset is usually in adulthood, and candidiasis is not present.

Details

• E31.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

• The 2023 edition of ICD-10-CM E31.0 became effective on October 1, 2022.

• This is the American ICD-10-CM version of E31.0 – other international versions of ICD-10 E31.0 may differ.