E76.03
Scheie’s syndrome
Approximate Synonyms
-
Mucopolysaccharidosis mps-i-s
Clinical Information
-
An autosomal recessive disorder representing the milder form of mucopolysaccharidosis type i. It is characterized by deficiency of the enzyme alpha-l-iduronidase. Signs and symptoms include broad mouth with full lips, cloudy cornea which may lead to blindness, stiff joints, and hirsutism.
Details
-
E76.03 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
-
The 2023 edition of ICD-10-CM E76.03 became effective on October 1, 2022.
-
This is the American ICD-10-CM version of E76.03 – other international versions of ICD-10 E76.03 may differ.