E88.41

Applicable To

• Mitochondrial myopathy, encephalopathy, lactic acidosis and stroke-like episodes

Approximate Synonyms

• Juvenile myopathy, encephalopathy, lactic acidosis and stroke

• Mitochondrial encephalopathy, lactic acidosis, stroke

Clinical Information

• A mitochondrial disorder characterized by focal or generalized seizures, episodes of transient or persistent neurologic dysfunction resembling strokes, and ragged-red fibers on muscle biopsy. Affected individuals tend to be normal at birth through early childhood, then experience growth failure, episodic vomiting, and recurrent cerebral insults resulting in visual loss and hemiparesis. The cortical lesions tend to occur in the parietal and occipital lobes and are not associated with vascular occlusion. Vascular headache is frequently associated and the disorder tends to be familial. from Joynt, Clinical Neurology, 1992, ch56, p117)

Details

• E88.41 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

• The 2023 edition of ICD-10-CM E88.41 became effective on October 1, 2022.

• This is the American ICD-10-CM version of E88.41 – other international versions of ICD-10 E88.41 may differ.