G60.0

Applicable To

• Charcot-Marie-Tooth disease

• Déjérine-Sottas disease

• Hereditary motor and sensory neuropathy, types I-IV

• Hypertrophic neuropathy of infancy

• Peroneal muscular atrophy axonal type) hypertrophic type)

• Roussy-Levy syndrome

Approximate Synonyms

• Charcot marie tooth disease

• Charcot marie tooth disease, type 1

• Charcot marie tooth disease, type 2

• Charcot marie tooth disease, type 3

• Charcot marie tooth disease, type 4

• Charcot-marie-tooth disease type 4

• Charcot-marie-tooth disease, type i

• Charcot-marie-tooth disease, type ii

• Dejerine sottas disease

• Dèjèrine-sottas disease

• Hereditary motor and sensory neuropathy with optic atrophy

• Neuropathy nerve damage) hereditary motor and sensory

Clinical Information

• A group of slowly progressive inherited disorders affecting motor and sensory peripheral nerves. Subtypes include hmsns i-vii. Hmsn i and ii both refer to charcot-marie-tooth disease. Hmsn iii refers to hypertrophic neuropathy of infancy. Hmsn iv refers to refsum disease. Hmsn v refers to a condition marked by a hereditary motor and sensory neuropathy associated with spastic paraplegia see spastic paraplegia, hereditary). Hmsn vi refers to hmsn associated with an inherited optic atrophy optic atrophies, hereditary), and hmsn vii refers to hmsn associated with retinitis pigmentosa. from Adams et al., Principles of Neurology, 6th ed, p1343)

• A hereditary motor and sensory neuropathy transmitted most often as an autosomal dominant trait and characterized by progressive distal wasting and loss of reflexes in the muscles of the legs and occasionally involving the arms). Onset is usually in the second to fourth decade of life. This condition has been divided into two subtypes, hereditary motor and sensory neuropathy hmsn) types i and ii. Hmsn i is associated with abnormal nerve conduction velocities and nerve hypertrophy, features not seen in hmsn ii. Adams et al., Principles of Neurology, 6th ed, p1343)

• A progressive hereditary disorder that causes nerve damage

• An inherited degenerative disorder involving the peripheral nerves. It is caused by mutations in the genes that are responsible for the production of proteins necessary for the function and structure of the peripheral nerves. It is characterized by muscle atrophy and weakness in the feet, legs, hands, and arms and loss of sensation in the limbs.

• Charcot-marie-tooth disease cmt) is a group of genetic nerve disorders. It is named after the three doctors who first identified it. In the United States, cmt affects about 1 in 3,300 people. Cmt affects your peripheral nerves. Peripheral nerves carry movement and sensation signals between the brain and spinal cord and the rest of the body. Symptoms usually start around the teen years. Foot problems such as high arches or hammertoes can be early symptoms. As cmt progresses, your lower legs may weaken. Later, your hands may also become weak. There is no cure. The disease can be so mild you don’t realize you have it or severe enough to make you weak. Many people with cmt lead active lives and have a normal life span. Physical therapy, occupational therapy, braces and other devices and sometimes surgery can help you cope. genetics home reference

• Group of peripheral nervous system hereditary disorders with varying course, symptoms, neuropathology, and genetics, but generally involving gradual loss of nerve conduction, distal wasting, deformity, and disability.

Details

• G60.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

• The 2023 edition of ICD-10-CM G60.0 became effective on October 1, 2022.

• This is the American ICD-10-CM version of G60.0 – other international versions of ICD-10 G60.0 may differ.