I27.89

Clinical Information

• A condition associated with ventricular septal defect and other congenital heart defects that allow the mixing of pulmonary and systemic circulation, increase blood flow into the lung, and subsequent responses to low oxygen in blood. This complex is characterized by progressive pulmonary hypertension; hypertrophy of the right ventricle; cyanosis; and erythrocytosis.

• A syndrome characterized by the reversal of a septal defect-associated left-to-right shunt due to the resulting secondary pulmonary hypertension. The presence of the pulmonary hypertension causes increased pressure in the right heart chambers resulting in the reversal of the shunt into a right-to-left shunt. Signs and symptoms include cyanosis, pulmonary hypertension, heart failure, and high red blood cell count.

Details

• I27.89 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

• The 2023 edition of ICD-10-CM I27.89 became effective on October 1, 2022.

• This is the American ICD-10-CM version of I27.89 – other international versions of ICD-10 I27.89 may differ.