J84.01

Approximate Synonyms

• Pulmonary alveolar proteinosis

Clinical Information

• A pulmonary alveoli-filling disease, characterized by dense phospholipoproteinaceous deposits in the alveoli, cough, and dyspnea. This disease is often related to, congenital or acquired, impaired processing of pulmonary surfactants by alveolar macrophages, a process dependent on granulocyte-macrophage colony-stimulating factor.

• A rare lung disorder characterized by the filling of the pulmonary alveoli with proteinaceous material which stains positive with periodic acid-schiff stain. It may be idiopathic or secondary due to hematologic malignancies or the inhalation of mineral dusts. Signs and symptoms include dyspnea, cough and low grade fever.

• Unknown etiology marked by chronic filling of alveoli with proteinaceous, lipid-rich, granular material consisting of surfactant and debris of necrotic cells.

Details

• J84.01 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

• The 2023 edition of ICD-10-CM J84.01 became effective on October 1, 2022.

• This is the American ICD-10-CM version of J84.01 – other international versions of ICD-10 J84.01 may differ.