K00.5

Applicable To

• Amelogenesis imperfecta

• Dentinogenesis imperfecta

• Odontogenesis imperfecta

• Dentinal dysplasia

• Shell teeth

Approximate Synonyms

• Hereditary disturbances in tooth structure

Clinical Information

• A clinically and genetically heterogeneous group of hereditary conditions characterized by malformed dental enamel, usually involving dental enamel hypoplasia and/or tooth hypomineralization.

• A congenital tooth development disorder caused by mutations in the dspp gene. The teeth are weak, discolored, and translucent.

• An apparently hereditary disorder of dentin formation, marked by a normal appearance of coronal dentin associated with pulpal obliteration, faulty root formation, and a tendency for peripheral lesions without obvious cause. from Dorland, 27th ed)

• An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.

Details

• K00.5 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

• Short description: Hereditary disturbances in tooth structure, NEC

• The 2023 edition of ICD-10-CM K00.5 became effective on October 1, 2022.

• This is the American ICD-10-CM version of K00.5 – other international versions of ICD-10 K00.5 may differ.