Blau syndrome
Deficiency of interleukin 1 receptor antagonist [DIRA]
Majeed syndrome
Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]
M04.8 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2023 edition of ICD-10-CM M04.8 became effective on October 1, 2022.
This is the American ICD-10-CM version of M04.8 – other international versions of ICD-10 M04.8 may differ.