D47.0

Approximate Synonyms

• Mastocytoma

• Neoplasm of uncertain behavior, histiocytic or mas

• Neoplasm of uncertain behavior, histiocytic or mast cell

Clinical Information

• A form of systemic mastocytosis in which patients experience no pain. It is characterized by the multifocal mast cell filtrates, mostly in skin and bone marrow <20% mast cells). It has a low cytomorphological grade.

• A growth or lump of mast cells a type of white blood cell). Mast cell tumors can involve the skin, subcutaneous tissue, and muscle tissue.

• A heterogeneous group of disorders characterized by the abnormal growth and accumulation of mast cells in one or more organ systems. Recent data suggest that most variants of mastocytosis are clonal disorders. who, 2001)

• A localized tumor composed of sheets of mast cells without atypia. It includes the cutaneous mastocytoma which involves the dermis and subcutaneous tissue, and the extracutaneous mastocytoma. Most cases of extracutaneous mastocytoma have been reported in the lung.

• A neoplasm composed of mast cells, for which the malignancy status has not been determined.

• An indolent mast cell neoplasm characterized by systemic infiltration of skin and internal organs by aggregates of neoplastic mast cells.

• An indolent mast cell neoplasm characterized by systemic infiltration of skin and internal organs by aggregates of neoplastic mast cells. There is no evidence of mast cell leukemia or clonal hematologic malignancy. Clinically, there is no evidence of palpable hepatomegaly and splenomegaly, malabsorption syndrome, or pathologic fractures.

• Nodular cutaneous mast cell infiltrate, which is usually present at birth or soon after as a solitary nodule, although three to four lesions may occur; lesions typical of urticaria pigmentosa may occur later.

Details

• D47.0 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.

• The 2023 edition of ICD-10-CM D47.0 became effective on October 1, 2022.

• This is the American ICD-10-CM version of D47.0 – other international versions of ICD-10 D47.0 may differ.