D56.0

Applicable To

• Alpha thalassemia major

• Hemoglobin H Constant Spring

• Hemoglobin H disease

• Hydrops fetalis due to alpha thalassemia

• Severe alpha thalassemia

• Triple gene defect alpha thalassemia

Approximate Synonyms

• Alpha^+^ thalassemia, deletion type

• Alpha^+^ thalassemia, nondeletion type

• Alpha^0^ thalassemia co-occurrent with deletional alpha^+^ thalassemia

• Alpha^0^ thalassemia co-occurrent with nondeletional alpha^+^ thalassemia

• Hgb h disease, deletion type

• Hgb h disease, nondeletion type

• Homozygous alpha thalassemia

• Thalassemia, alpha

• Thalassemia, alpha plus, deletion type

• Thalassemia, alpha plus, nondeletion type

• Thalassemia, alpha, homozygous

Clinical Information

• A disorder characterized by reduced synthesis of the alpha chains of hemoglobin. The severity of this condition can vary from mild anemia to death, depending on the number of genes deleted.

• A genetic hematologic disorder characterized by partial or complete absence of the alpha globin chains of the heme molecule.

Details

• D56.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

• The 2023 edition of ICD-10-CM D56.0 became effective on October 1, 2022.

• This is the American ICD-10-CM version of D56.0 – other international versions of ICD-10 D56.0 may differ.